Biventricular Repair in Double Outlet Right Ventricle with Non-Committed VSD: Impossible To Possible

Abstract

Double outlet right ventricle is a relatively uncommon cyanotic congenital heart disease. The most simple meaning of DORV is the origin of both the aorta and pulmonary artery is from the right ventricle. But, in reality, DORV  is full of complexities. Its clinical spectrum spans from VSD-like presentation to TOF to TGA. Biventricular repair is the treatment of choice for DORV-committed VSD with or without pulmonary stenosis with excellent results but the surgical treatment of DORV non-committed VSD remained controversial. Because of the technical challenges, the common surgical strategy for DORV non-committed VSD is a single ventricle pathway. Now, with an understanding of the anatomy and physiology of this subset, gradually these difficulties in surgical repair are being overcome. This review article will enlighten the various methods of biventricular repair of DORV non-committed VSD with and without pulmonary stenosis and condensing the indications for univentricular repair to a very limited space.